Intrathoracic desmoid tumors are very rare. We report a case of a 35-year-old woman, who had dyspnea and dysphagia. The imaging studies
showed a voluminous mass tissue occupying the thoracic outlet and extending to the medium mediastinum. A scanno-guided percutaneous needle
biopsy initially concluded to a solitary fibrous tumor of the pleura. Surgery was decided. The approach of this voluminous apical and intra thoracic
mass was challenging. Complete resection was successfully performed by Cormier Dartevelle Grunenwald’s route. Final pathology was consistent
with desmoid fibromatosis. The post-operative course was uneventful.