Kikuchi-Fujimoto Disease (KFD) typically presents as cervical lymphadenopathy in young healthy women. Cervical lymph node involvement has been found in almost all of the previous studies, axillary lymph node involvement, however, was reported only in one out of eight cases reported from Nepal. In the 11 cases reported from India, all of them involved the cervical lymph nodes. In a retrospective study of 195 patients by Cheng et al., only 2.6% only had involvement of axillary lymph nodes. Here we report a case of a 21-year-old male who presented with fever and right-sided axillary lymphadenopathy. Furthermore, in contrast to the typical presentation, the patient had a normal Erythrocyte sedimentation rate, thrombocytopenia and tested negative for EBV.