Journal of Clinical Case Reports

Malignant Peripheral Nerve Sheath Tumor in Parotid Gland-A Rare and Challenging Case

Abstract

Priyadarshini Biswa, Asaranti Kar, Lity Mohanty, Kaumudee Pattnaik and Manjushree Nayak

Malignant peripheral nerve sheath tumor accounts for about <10% of all sarcomas. It’s incidence in the parotid gland is even rarer. A 49 year old male presented to the ENT department with a history of parotid swelling of 1 year duration. The mass was rapidly increasing in size. We received the gross specimen comprising of irregular, grayish white tissue in pieces, as the tumor was infiltrating into the deeper structures and couldn’t be removed in toto. Histomorphological features showed a spindle cell neoplasm with features of malignant peripheral nerve sheath tumour. Neural origin of the tumor was confirmed by immunohistochemistry. The patient is now receiving radiotherapy and doing well. We report this case due to its rarity and also to aware the surgical pathologists to keep this as a differential diagnosis in the evaluation of all spindle cell parotid tumours.